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Abstract
Epithelioid inflammatory myofibroblastic sarcoma (EIMS), known as a scarce variant of the inflammatory myofibroblastic tumor (IMT), is characterized by distinctive morphology, nuclear membrane staining of ALK, and ALK gene fusion. Herein, we present a rare case of EIMS, appearing as an abdominal mass of an 8-year-old girl. The mass was next to the bladder and was indicated to be removed by surgery. With the pathological diagnosis of EIMS, the patient received adjuvant treatment with ALK inhibitor. To the best of our knowledge, the case is potentially the first instance of EIMS in a Vietnamese child. Given the rarity and aggressive clinical course of EIMS, clinicians’ and pathologists’ familiarity with its clinicopathological and molecular characteristics can be crucial for diagnosis.
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| Published | 23-12-2024 | |
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| Issue | Vol. 16 No. 6 (2024) | |
| Section | Case report | |
| DOI | 10.38103/jcmhch.16.6.12 | |
| Keywords | Sarcoma nguyên bào xơ cơ viêm dạng biểu mô, ALK, trẻ em Epithelioid inflammatory myofibroblastic sarcoma, ALK, child |
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