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Abstract
Background: Congenital sensorineural hearing loss due to inner ear malformations is approximately 1 in 3800 childbirths. There were bilateral malformations in 15 - 20% of the cases. Imaging plays an important evaluation in the detection and classification of inner ear malformations. We present a 30 - month - old female with cochlear aplasia on the right side and cochlear hypoplasia type 2 on the left side diagnosed at Vinmec Times City Hospital.
Case report: A female 30 - month - old has been examined at Vinmec Times City Hospital due to her low response to sounds. She has performed Temporal Bone Computed Tomography (CT) and Magnetic Resonance Imaging (MRI) of the inner ear to assess the ear structure and brain parenchyma. On CT and MRI images, presence of cochlear aplasia and cochlear nerve aplasia on the right side, hypoplasia of cochlear (type 2) and cochlear nerve on the left side, and decision was made not to implant surgery due to high risk of failure.
Conclusion: Temporal Bone CT and Inner Ear MRI have an essential role in the diagnosis of inner ear malformations and help with surgical decisions making whether a cochlear implant is indicated or not and estimating the success rate
References
Korver A.M.H., Smith R.J.H., Van Camp G. và cộng sự. Congenital hearing loss. Nat Rev Dis Primer. 2017;3:16094.
Joshi V.M., Navlekar S.K., Kishore G.R. và cộng sự. CT and MR Imaging of the Inner Ear and Brain in Children with Congenital Sensorineural Hearing Loss. RadioGraphics. 2012; 32(3): 683-698.
Yiin R.S.Z., Tang P.H., và Tan T.Y. Review of congenital inner ear abnormalities on CT temporal bone. Br J Radiol. 2011; 84:859-863.
AL Sheikh M. Cochlear Apalsia and Cochlear Hypoplasia Incidental CT Finding A Case Report. Glob J Otolaryngol. 2017;12(1).
Mazón M., Pont E., Montoya-Filardi A. và cộng sự.Inner ear malformations: A practical diagnostic approach. 2016; 9.
Sennaroglu L., Sennaroglu G., và Atay G. Auditory Brainstem Implantation in Children. Curr Otorhinolaryngol Rep. 2013;1(2): 80-91.
Quirk B., Youssef A., Ganau M. và cộng sự. Radiological diagnosis of the inner ear malformations in children with sensorineural hearing loss. BJR|Open. 2019; 1(1): 20180050.
Swartz J.D. và Loevner L.A., btv.Imaging of the temporal bone.Thieme, New York Stuttgart.2009; 312(12): 605
Freeman S.R. và Sennaroglu L. Management of Cochlear Nerve Hypoplasia and Aplasia. Advances in Oto-Rhino-Laryngology. S. Karger AG. 2018; 81-92.
Sennaroglu L. Cochlear Implantation in Inner Ear Malformations - A Review Article. Cochlear Implants Int. 2010;11(1): 4-41.
Cinar B.C., Batuk M.O., Tahir E. và cộng sự. Audiologic and radiologic findings in cochlear hypoplasia. Auris Nasus Larynx.2017; 44(6):
-663.
Clemmens C.S., Guidi J., Caroff A. và cộng sự. Unilateral Cochlear Nerve Deficiency in Children. Otolaryngol Neck Surg. 2013;149(2):
-325.
| Published | 08-01-2025 | |
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| Issue | No. 73 (2021) | |
| Section | Original article | |
| DOI | 10.38103/jcmhch.2021.73.1 | |
| Keywords | Từ khoá: Dị dạng tai trong, bất sản ốc tai, thiểu sản ốc tai. Keywords: Inner ear malformation, cochlear aplasia, cochlear hypoplasia. |
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