Abstract

Objectives: To evaluate the clinical outcomes of care for diffused cutaneous and mucosal lesions in a case of Paraneoplastic Pemphigus, a rare life-threatening autoimmune skin disease.

Case report: A 19-year-old male patient had a large retroperitoneal tumor measuring 136x65x131mm, compressing surrounding organs. He was admitted to the Dermatology and Burns Department of Bach Mai Hospital for treatment with severe thinness, oral and lip mucosal ulcers, widespread skin lesions. The damaged area accounted for more than 80% of the body surface area. The patient was then diagnosed with paraneoplastic pemphigus and was indicated for surgical removal of the tumor when clinical conditions permitted.

Conclusions: After nearly 200 days of hospitalization, with the support of a multidisciplinary team, especially the comprehensive and dedicated care strategy of the nursing team. The patient underwent major surgery to remove the tumor and fully recovered after the operation. This is the report of care for diffused cutaneous and mucosal lesions in a rare case of paraneoplastic pemphigus first recorded in Vietnamese medical literature.