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Abstract
Objectives: Pseudomyogenic hemangioendothelioma (PH) is amalignant mesenchymal tumor which
is extremely rare in neonate. We report an unusual case with PH on cheek in a neonate, which is the first
case published till date.
Case study: A 40-day-old female infant presented to hospital with a lesion on her right cheek appearing
right after delivery, mimicking a hemangioma but rapidly increasing in size over the time. Clinical examination
along with radiography (ultrasound and computed tomography) suggested diagnosis of fibrosarcoma. The
patient was taken to surgery to resect the tumor along withconserve facial nerve branches. Histology and
immunohistochemistry results were suitable with PH diagnosis. The patient is in recovery period and is
followed up.
Conclusion: PH is extremely rare in children. Clinicians should consider this diagnosis when
approaching an abnormal mass occurring in children, especially in unusual locations, to achieve the best
plan in treatment.
Keywords: Pseudomyogenic hemangioendothelioma, epithelioid sarcoma, face, facial nerve.
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Copyright (c) 2019 Journal of Clinical Medicine Hue Central Hospital