Tóm tắt
Objectives: To evaluate the results of corticosteroids and vincristine in the management of Kaposiformhemangioendothelioma(KHE) with Kasabach-Merritt syndrome.
Materials and Methods: Case series review.
Results: Six cases had KHE with Kasabach-Merritt syndrome and were treated by corticosteroids in combination with vincristine. The complete response, partial response and no apparent response were achieved at 50%, 33.3% and 16.7% among the study group respectively. Vincristine had mild and transient side effects compared to corticosteroids.
Conclusion: Corticosteroids and vincristine may be first-line therapy in the management of KHE with Kasabach-Merritt syndrome.
Tài liệu tham khảo
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